Garcia Pavia, Pablo pablo.garciap@uam.es
Actividades
- Artículos 404
- Libros 0
- Capítulos de libro 9
- Congresos 81
- Documentos de trabajo 1
- Informes técnicos 2
- Proyectos de investigación 0
- Tesis dirigidas 15
- Patentes o licencias de software 0
Efficacy of Acoramidis in Wild-Type and Variant Transthyretin Amyloid Cardiomyopathy: Results From ATTRibute-CM and Its Open-Label Extension
- Alexander KM
- Davis MK
- Akinboboye O
- Berk J
- Bhatt K
- Cappelli F
- Cuddy SAM
- Fontana M
- Garcia-Pavia P
- Gillmore JD
- Griffin JM
- Grodin JL
- Judge DP
- Khouri MG
- Lam K
- Masri A
- Maurer MS
- Obici L
- Ruberg FL
- Sarswat N
- Shah K
- Soman P
- Stern L
- Wright R
- Xiong K
- Cao X
- Lystig T
- Tamby JF
- Castaño A
- Katz L
- Sinha U
- Fox JC
- Solomon SD
- Grogan M
Jama Cardiology - 1/1/2026
10.1001/jamacardio.2025.4477 Ver en origen
- ISSN 23806583
Early Access to Tafamidis for Patients With Transthyretin Amyloid Cardiomyopathy
- Crespo-Leiro, Maria G
- Hanna, Mazen
- Damy, Thibaud
- Delgado, Diego
- Ebede, Ben
- Marino, Valentina
- Wang, Ronnie
- Maurer, Mathew S
- Garcia-Pavia, Pablo
- Drachman, Brian M
Jacc: Advances - 10/9/2025
10.1016/j.jacadv.2025.102122 Ver en origen
- ISSN 2772963X
Clinical care of family members of patients with dilated cardiomyopathy
- Verdonschot, Job A J
- Kaski, Juan Pablo
- Asselbergs, Folkert W
- Behr, Elijah R
- Charron, Philippe
- Dawson, Dana
- Haugaa, Kristina H
- Kuchynka, Petr
- Lopes, Luis R
- Mazzanti, Andrea
- Monserrat, Lorenzo
- Pantazis, Antonis
- Prasad, Sanjay K
- Schunkert, Heribert
- Seferovic, Petar M
- Sheppard, Mary N
- Sinagra, Gianfranco
- van Tintelen, J Peter
- Tome Esteban, Maria Teresa
- Heymans, Stephane R B
- Garcia-Pavia, Pablo
European Heart Journal (p. 4569-4582) - 3/9/2025
10.1093/eurheartj/ehaf571 Ver en origen
- ISSN 15229645
Hereditary transthyretin amyloidosis caused by the Val142Ile variant in Spain
- de Frutos F
- Herrador L
- Peiró-Aventín B
- Eiros R
- Limeres Freire J
- Zorio E
- Carbayo Á
- Llongueras-Espí P
- García-Álvarez A
- Ripoll-Vera T
- Macías R
- Vilches S
- Ruiz-Bustillo S
- Arana-Achaga X
- Gayán Ordás J
- Piqueras-Flores J
- Ruiz-Cueto M
- Casasnovas C
- Tirón C
- Rojas-García R
- Sevilla T
- Rodríguez-Palomares JF
- González-López E
- Villacorta E
- García-Pavía P
- González-Costello J
Revista Española De Cardiología (p. 768-777) - 1/9/2025
10.1016/j.recesp.2024.12.016 Ver en origen
- ISSN 03008932
Genetic and Phenotypic Characterization of Nexilin (NEXN)–Related Cardiomyopathy: Results From a Multicentric Study
- Perotto M
- Paldino A
- Mazzarotto F
- Barbati G
- Stroeks SLVM
- Verdonschot JAJ
- Akhtar M
- Elliott P
- Ochoa JP
- Garcia-Pavia P
- de Frutos F
- Sepp R
- Hategan L
- Prasad S
- Yazdani M
- Morris-Rosendahl D
- Palinkas ED
- Girolami F
- Olivotto I
- Parikh VN
- Fatkin D
- Lakdawala N
- McKenna WJ
- Stolfo D
- Gigli M
- Brun F
- Collesi C
- Giacca M
- Zacchigna S
- Severini GM
- Lenarduzzi S
- Spedicati B
- Santin A
- Girotto G
- Gasparini P
- Taylor MRG
- Mestroni L
- Merlo M
- Sinagra G
- Dal Ferro M
Jacc-Heart Failure - 1/9/2025
10.1016/j.jchf.2025.102529 Ver en origen
- ISSN 22131779
CRISPR activation to repair electrocardiogram abnormalities caused by a FLNC truncating variant in mice
- Canas-Alvaro, Rodrigo
- Lalaguna, Laura
- Rubio, Blanca
- Ausiello, Antonella
- Lopez-Olaneta, Marina
- Serrano-Blanco, Rocio F
- Ochoa, Juan Pablo
- de la Pompa, Jose Luis
- Chavez, Alejandro
- Garcia-Pavia, Pablo
- Lara-Pezzi, Enrique
European Heart Journal (p. 4610-4613) - 31/8/2025
10.1093/eurheartj/ehaf703 Ver en origen
- ISSN 15229645
Mavacamten in Symptomatic Nonobstructive Hypertrophic Cardiomyopathy
- Desai, Milind Y
- Owens, Anjali T
- Abraham, Theodore
- Olivotto, Iacopo
- Garcia-Pavia, Pablo
- Lopes, Renato D
- Elliott, Perry
- Fernandes, Fabio
- Verheyen, Nicolas
- Maier, Lars
- Meder, Benjamin
- Azevedo, Olga
- Kitaoka, Hiroaki
- Wolski, Kathy
- Wang, Qiuqing
- Jaber, Wael
- Mitchell, Lisa
- Myers, Jonathan
- Rano, Thomas
- Gong, Zhiqun
- Zhong, Yue
- Carter-Bonanza, Suzanne
- Florea, Victoria
- Aronson, Ron
- Nissen, Steven E
New England Journal Of Medicine (p. 961-972) - 30/8/2025
10.1056/nejmoa2505927 Ver en origen
- ISSN 15334406
Aficamten or Metoprolol Monotherapy for Obstructive Hypertrophic Cardiomyopathy
- Garcia-Pavia, Pablo
- Maron, Martin S
- Masri, Ahmad
- Merkely, Bela
- Nassif, Michael E
- Pena-Pena, Maria Luisa
- Barriales-Villa, Roberto
- Bilen, Ozlem
- Burroughs, Melissa
- Claggett, Brian
- Costabel, Juan Pablo
- Correia, Edileide de Barros
- Dybro, Anne M
- Elliott, Perry
- Hegde, Sheila M
- Lakdawala, Neal K
- Lewis, Gregory D
- Mann, Amy
- Miao, Zi Michael
- Nair, Ajith
- Poulsen, Steen H
- Reant, Patricia
- Schulze, P Christian
- Solomon, Scott D
- Wang, Andrew
- Sohn, Regina
- Berhane, Indrias
- Heitner, Stephen B
- Jacoby, Daniel L
- Kupfer, Stuart
- Malik, Fady I
- Wohltman, Amy
- Fifer, Michael A
New England Journal Of Medicine (p. 949-960) - 30/8/2025
10.1056/nejmoa2504654 Ver en origen
- ISSN 15334406
Vutrisiran in Transthyretin Amyloidosis A Pooled Safety Analysis of HELIOS-A and HELIOS-B
- Witteles, Ronald M
- Garcia-Pavia, Pablo
- Morbach, Caroline
- Gillmore, Julian D
- Taylor, Mark S
- Conceicao, Isabel
- White, William B
- Kwok, Cynthia
- Sweetser, Marianne T
- Boyle, Katherine L
- Adams, David
Jacc: Advances - 22/8/2025
10.1016/j.jacadv.2025.102066 Ver en origen
- ISSN 2772963X
Contemporary practice and resource availability for genetic testing in paediatric hypertrophic cardiomyopathy
- Sandmann C
- Klaassen S
- Kaski JP
- Norrish G
- Adwani S
- Anastasakis A
- Andersen NH
- Baban A
- Barriales-Villa R
- Biagni E
- Bharucha T
- Bhole V
- Brugada GS
- Bruyndonckx L
- Bokenkamp R
- Castro F
- Chaker M
- Centeno F
- Daubeney P
- Wilde HD
- Donne GD
- Fernández A
- Garcia-Pavia P
- Gran F
- Grech V
- Guereta LG
- Lemcke MSG
- Khodaghalian B
- Kaski JP
- Khraiche D
- Klaassen S
- Kovacevic A
- Kubo T
- Kubus P
- Limongelli G
- Linter K
- López CM
- Luczak-Wozniak K
- Marrone C
- Mathur S
- Mcleod K
- Miranda JO
- Mogensen J
- Norrish G
- Ojala T
- Olivotto I
- Perin F
- Popoiu A
- Prendiville T
- Rădulescu CR
- Raimondi F
- Reinhardt Z
- Sandmann C
- Schouvey S
- Sinagra G
- Smedsrud MK
- Spentzou G
- Tchana B
- Tejeira MMS
- Uzun O
- Weintraub R
- Wolf C
- Yamazawa H
- Ziolkowski L
Journal Of Medical Genetics (p. 528-530) - 1/8/2025
10.1136/jmg-2025-110696 Ver en origen
- ISSN 00222593
Este/a investigador/a no tiene libros.
From Red Flags to Diagnosis
- Gillmore JD
- Aimo A
- Garcia-Pavia P
Cardiac Amyloidosis Diagnosis And Treatment (p. 197-207) - 1/1/2024
The coronary circulation in cardiomyopathies and cardiac allografts: Effect of specific pathologies on epicardial vessels and the microcirculation
- Broyd C
- Dominguez F
- Garcia-Pavia P
Physiological Assessment Of Coronary Stenoses And The Microcirculation (p. 119-135) - 10/8/2017
Clinico-Pathological Atlas of Cardiovascular Diseases
- Lucena JS
- García-Pavía P
- Suárez-Mier MP
- Alonso-Pulpón LA
Clinico Pathological Atlas Of Cardiovascular Diseases (p. 1-362) - 1/1/2014
Cardiomyopathies
- Aguilera B
- Suárez-Mier MP
- Guzzo-Merello G
- García-Pavía P
Clinico Pathological Atlas Of Cardiovascular Diseases (p. 201-231) - 1/1/2014
Pathology of the Pericardium
- Molina P
- Aguilera B
- Cobo M
- García-Pavía P
Clinico Pathological Atlas Of Cardiovascular Diseases (p. 91-107) - 1/1/2014
Cardiovascular Pathology Secondary to Alcohol Consumption, Drugs of Abuse and Medication
- Lucena JS
- Garamendi PM
- Guzzo-Merello G
- García-Pavía P
Clinico Pathological Atlas Of Cardiovascular Diseases (p. 299-316) - 1/1/2014
Pathology of the Heart Valves
- Suárez-Mier MP
- Morentin B
- Cobo M
- Castedo E
- García-Pavía P
Clinico Pathological Atlas Of Cardiovascular Diseases (p. 171-200) - 1/1/2014
Trasplante cardíaco: indicaciones
- García Pavía, Pablo
- Gómez Bueno, Manuel F
- Segovia, Javier
- Pulpón Rivera, Luis Alonso
Cuidados Críticos: Protocolos (p. 1093-1097) - 1/1/2013
- iMarina
ACORAMIDIS IMPROVES CLINICAL OUTCOMES IN PATIENTS WITH TRANSTHYRETIN AMYLOID CARDIOMYOPATHY: A POST HOC RECURRENT EVENT ANALYSIS OF ATTRIBUTE-CM STUDY
- Judge, Daniel p
- Alexander, Kevin m
- Cappelli, Francesco
- Fontana, Marianna
- Garcia-pavia, Pablo
- Gibbs, Simon
- Grogan, Martha
- Hanna, Mazen
- Masri, Ahmad
- Maurer, Mathew
- Obici, Laura
- Soman, Prem
- Cao, Xiaofan (martha)
- Wang, Kevin
- Tamby, Jean-francois
- Siddhanti, Suresh
- Fox, Jonathan
- Gillmore, Julian
Journal Of Cardiac Failure - 1/1/2025
- ISSN 10719164
- iMarina
Design and rationale for MAGNITUDE, a phase 3, randomized, placebo-controlled trial of NTLA2001, a CRISPR-based gene editing therapy, in patients with transthyretin amyloidosis with cardiomyopathy (ATTR- CM)
- Maurer, Mathew S
- Fontana, Marianna
- Claggett, Brian
- Hernandez, Adrian
- Januzzi, James L
- Lam, Carolyn
- Lewis, Eldrin
- Garcia-Pavia, Pablo
- Shah, Sanjiv J
- Solomon, Scott
- Gutstein, David
- Pickard, Michael D
- Anderson, Lisa
- Olbertz, Joy
Amyloid-Journal Of Protein Folding Disorders (p. S60-S60) - 23/5/2024
- ISSN 13506129
- iMarina
In vivo AAV based gene therapy reduces cardiac conduction defects in TMEM43 mediated arrhythmogenic cardiomyopathy
- Lalaguna, L
- Lopez-Olaneta, M
- Villalba-Orero, M
- Garcia-Pavia, P
- Lara-Pezzi, E
Human Gene Therapy (p. A257-A257) - 1/2/2024
- ISSN 10430342
- iMarina
Acoramidis Reduces All-Cause Mortality (ACM) and Cardiovascular-Related Hospitalization (CVH): Initial Outcomes From the ATTRibute-CM Open-Label Extension (OLE)
- Judge, Daniel
- Gillmore, Julian
- Alexander, Kevin
- Ambardekar, Amrut
- Cappelli, Francesco
- Fontana, Marianna
- Garcia-Pavia, Pablo
- Grogan, Martha
- Hanna, Mazen
- Masri, Ahmad
- Obici, Laura
- Poulsen, Steen
- Sarswat, Nitasha
- Shah, Keyur
- Soman, Prem
- Cao, Xiaofan
- Wang, Kevin
- Pecoraro, Maria
- Tamby, Jean-Francois
- Katz, Leonid
- Fox, Jonathan
- Maurer, Mathew
Circulation (p. E739-E740) - 17/12/2024
- ISSN 00097322
- iMarina
Efficacy and Safety of Aficamten in Patients Guideline-Eligible for Septal Reduction Therapy in the FOREST-HCM Trial
- Masri, Ahmad
- Choudhury, Lubna
- Garcia-Pavia, Pablo
- Abraham, Theodore
- Barriales-Villa, Roberto
- Bilen, Ozlem
- Elliott, Perry
- Hagege, Albert
- Nagueh, Sherif
- Naidu, Srihari
- Nassif, Michael
- Olivotto, Iacopo
- Oreziak, Artur
- Owens, Anjali
- Wever-Pinzon, Omar
- Rader, Albree Tower
- Heitner, Stephen
- Kupfer, Stuart
- Malik, Fady
- Melloni, Chiara
- Meng, Lixin
- Wei, Jenny
- Saberi, Sara
Circulation - 12/11/2024
10.1161/circ.150.suppl_1.4142906 Ver en origen
- ISSN 00097322
Integrated safety and tolerability of mavacamten treatment over 5 years in patients with obstructive hypertrophic cardiomyopathy
- Owens, Anjali
- Barriales-Villa, Roberto
- Desai, Milind
- Garcia-Pavia, Pablo
- Hagege, Albert
- Olivotto, Iacopo
- Wojakowski, Wojtek
- Afsari, Sonia
- Balaratnam, Ganesh
- Chen, Yu Mao
- Wang, Andrew
Circulation - 12/11/2024
10.1161/circ.150.suppl_1.4134320 Ver en origen
- ISSN 00097322
Changes in EQ-5D-5L with Aficamten in Obstructive Hypertrophic Cardiomyopathy (oHCM): the SEQUOIA-HCM Trial
- Schulze, Christian
- Abraham, Theodore
- Barriales-Villa, Roberto
- Claggett, Brian
- Coats, Caroline
- Garcia-Pavia, Pablo
- Hagege, Albert
- Januzzi, James
- Kulac, Ian
- Kwong, Raymond
- Maron, Martin
- Masri, Ahmad
- Nassif, Michael
- Olivotto, Iacopo
- Spertus, John
- Veselka, Josef
- Jacoby, Daniel
- Kupfer, Stuart
- Malik, Fady
- Meng, Lixin
- Shreay, Sanatan
- Wohltman, Amy
- Maurer, Mathew
Circulation - 12/11/2024
10.1161/circ.150.suppl_1.4140102 Ver en origen
- ISSN 00097322
Sex-related Differences In Cardiac Involvement In Wild-type Transthyretin Amyloidosis
- Campbell, Courtney
- Lorusso, Samantha
- Dispenzieri, Angela
- Kristen, Arnt
- Maurer, Mathew S.
- Rapezzi, Claudio
- Lairez, Olivier
- Drachman, Brian
- Garcia-Pavia, Pablo
- Grogan, Martha
- Chapman, Doug
- Amass, Leslie;
Journal Of Cardiac Failure (p. S111-S111) - 1/4/2022
- ISSN 10719164
- iMarina
HELIOS-A: 18-MONTH EXPLORATORY CARDIAC RESULTS FROM THE PHASE 3 STUDY OF VUTRISIRAN IN PATIENTS WITH HEREDITARY TRANSTHYRETIN-MEDIATED AMYLOIDOSIS
- Mussinelli, Roberta
- Garcia-pavia, Pablo
- Gillmore, Julian D.
- Kale, Parag
- Berk, John L.
- Maurer, Mathew S.
- Conceicao, Isabel
- Dicarli, Marcelo
- Solomon, Scott
- Chen, Chongshu
- Arum, Seth
- Vest, John
- Grogan, Martha;
European Heart Journal Supplements - 1/12/2022
10.1093/eurheartjsupp/suac121.654 Ver en origen
- ISSN 1520765X
Natural History, Penotypes and Clinical Outcomes in Desmin Related Arrhythmogenic Cardiomyopathy
- Bermudez-Jimenez, Francisco Jose
- Protonotarios, Alexandros
- Rampazzo, Alessandra
- Zorio, Esther
- Brodehl, Andreas
- Arias, Miguel Angel
- Armenta, Juan Fernandez
- Macias-Ruiz, Rosa
- Garcia-Pavia, Pablo
- Gimeno, Juan Ramon
- Lopes, Luis R.
- Elliott, Perry M.
- Jimenez-Jaimez, Juan;
Circulation - 8/11/2022
- ISSN 00097322
- iMarina
Miectomía apical en pacientes con miocardiopatía hipertrófica apical e insuficiencia cardiaca avanzada
- Forteza, Alberto
- Esteban de Villareal, Juan
- Esteban Martin, Carlos
- Mingo, Susana
- Garcia-Suarez, Jessica
- Garcia-Pavia, Pablo
Revista Espanola De Cardiologia (p. 554-555) - 1/1/2021
10.1016/j.rec.2020.11.021 Ver en origen
- ISSN 03008932
- iMarina
- iMarina
Phase 1 Trial of Antibody NI006 for Depletion of Cardiac Transthyretin Amyloid
- Garcia-Pavia, Pablo
- Siepen, Fabian aus dem
- Donal, Erwan
- Lairez, Olivier
- van der Meer, Peter
- Kristen, Arnt V
- Mercuri, Michele F
- Michalon, Aubin
- Frost, Robert J A
- Grimm, Jan
- Nitsch, Roger M
- Hock, Christoph
- Kahr, Peter C
- Damy, Thibaud
New England Journal Of Medicine (p. 239-250) - 20/5/2023
10.1056/nejmoa2303765 Ver en origen
- ISSN 15334406
Phase 2 Study of Aficamten in Patients With Obstructive Hypertrophic Cardiomyopathy
- Maron, Martin S
- Masri, Ahmad
- Choudhury, Lubna
- Olivotto, Iacopo
- Saberi, Sara
- Wang, Andrew
- Garcia-Pavia, Pablo
- Lakdawala, Neal K
- Nagueh, Sherif F
- Rader, Florian
- Tower-Rader, Albree
- Turer, Aslan T
- Coats, Caroline
- Fifer, Michael A
- Owens, Anjali
- Solomon, Scott D
- Watkins, Hugh
- Barriales-Villa, Roberto
- Kramer, Christopher M
- Wong, Timothy C
- Paige, Sharon L
- Heitner, Stephen B
- Kupfer, Stuart
- Malik, Fady I
- Meng, Lisa
- Wohltman, Amy
- Abraham, Theodore
Journal Of The American College Of Cardiology (p. 34-45) - 3/1/2023
10.1016/j.jacc.2022.10.020 Ver en origen
- ISSN 07351097
Este/a investigador/a no tiene proyectos de investigación.
Penetrancia de miocardiopatía dilatada en familiares portadores genéticos sin fenotipo
- Gonzalez Mirelis, Jesus (Director)
- Garcia Pavia, Pablo (Director) Doctorando: Cabrera Romero, Eva
25/3/2025
- iMarina
Historia natural de la miocardiopatía dilatada por variantes en el gen de la cadena pesada de miosina beta (MYH7)
- Domínguez Rodríguez, Fernando (Director)
- Garcia Pavia, Pablo (Director) Doctorando: Frutos Seminario, Fernando de
16/9/2024
- iMarina
Variantes genéticas asociadas con la miocardiopatía dilatada inducida por quimioterapia
- Pablo García Pavía (Director) Doctorando: María Alejandra Restrepo Córdoba
20/12/2021
- iMarina
Papel del ventrículo derecho valorado por ecocardiografía bidimensional en el diagnóstico y pronóstico de la amiloidosis cardíaca por cadenas ligeras.
- Garcia Pavia, Pablo (Autor o Coautor)
- Tuñon Fernandez, Jose Luis (Autor o Coautor)
- Segovia Cubero, Javier (Director)
- Mingo Santos, Susana (Director) Doctorando: Durante López, Alejandro
22/9/2020
- iMarina
Prevalencia de amiloidosis cardiaca por transtiretina en pacientes con insuficiencia cardiaca con fracción de eyección preservada sin hipertrofia ventricular izquierda
- ACEÑA NAVARRO, ALVARO (Director)
- Ibáñez Cabeza, Borja (Director) Doctorando: Devesa Arbiol, Ana
1/1/2020
- iMarina
Aplicaciones de la genética a la cardiología clínica: hipercolesterolemia familiar y miocardiopatía dilatada alcohólica
- (Director)
- Pablo García Pavía (Director)
- Alonso-Pulpon Rivera, Luis Antonio (Tutor) Doctorando: María Almudena Amor Salamanca
17/12/2018
- iMarina
Aspectos clínicos y terapéuticos poco conocidos de la miocardiopatía hipertrófica: Endocarditis infecciosa y uso de anticoagulantes directos
- Alonso-Pulpon Rivera, Luis Antonio (Autor o Coautor)
- Pablo García Pavía (Director) Doctorando: Domínguez Rodríguez, Fernando
25/9/2017
- iMarina
Endocarditis infecciosa en pacientes con prolapso valvular mitral y válvula aórtica bicúspide
- Ramos Martinez, Antonio (Autor o Coautor)
- Alonso-Pulpon Rivera, Luis Antonio (Autor o Coautor)
- Pablo García Pavía (Director)
- Javier Segovia Cubero (Director) Doctorando: Isabel Zegrí
1/1/2017
- iMarina
Nuevos modelos preclínicos en insuficiencia cardiaca: caracterización con técnicas de imagen avanzada y aplicación en nuevas terapias
- Garcia Pavia, Pablo (Autor o Coautor)
- Rubio Campal, Jose Manuel (Autor o Coautor)
- Ibanez, Borja (Director)
1/1/2017
- iMarina
Caracterización clínica y genética de la miocardiopatía restrictiva idiopática
- Garcia Pavia, Pablo (Autor o Coautor)
- Segovia Cubero, Javier (Autor o Coautor)
- Alonso-Pulpon Rivera, Luis Antonio (Director) Doctorando: Gallego Delgado, María
22/4/2016
- iMarina
Este/a investigador/a no tiene patentes o licencias de software.
Perfiles de investigador/a
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ORCID
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Scopus Author ID
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Dialnet id

