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Clemente Perez, Paula paula.clemente@uam.es

Bioquímica / Universidad Autónoma de Madrid

Publications

Glutamyl-tRNAGln amidotransferase is essential for mammalian mitochondrial translation in vivo

  • Echevarría L
  • Clemente P
  • Herńandez-Sierra R
  • Gallardo M
  • Ferńandez-Moreno M
  • Garesse R

Biochemical Journal (p. 91-101) - 15/5/2014

10.1042/bj20131107 View at source

  • ISSN 02646021

Human COA3 Is an Oligomeric Highly Flexible Protein in Solution

  • Neira JL
  • Martínez-Rodríguez S
  • Hernández-Cifre JG
  • Cámara-Artigas A
  • Clemente P
  • Peralta S
  • Fernández-Moreno MÁ
  • Garesse R
  • García De La Torre J
  • Rizzuti B
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Biochemistry (p. 6209-6220) - 15/11/2016

10.1021/acs.biochem.6b00644 View at source

  • ISSN 00062960

Modeling human mitochondrial diseases in flies

  • Sánchez-Martínez A
  • Luo N
  • Clemente P
  • Adán C
  • Hernández-Sierra R
  • Ochoa P
  • Fernández-Moreno M
  • Kaguni L
  • Garesse R
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Biochimica Et Biophysica Acta-Bioenergetics (p. 1190-1198) - 1/9/2006

10.1016/j.bbabio.2006.05.008 View at source

  • ISSN 00052728

Evaluation of mitochondrial function and metabolic reprogramming during tumor progression in a cell model of skin carcinogenesis

  • Vallejo C., Cruz-Bermúdez A., Clemente P., Hernández-Sierra R., Garesse R., Quintanilla M.

Biochimie (p. 1171-1176) - 1/6/2013

10.1016/j.biochi.2013.01.001 View at source

  • ISSN 03009084

A multi-systemic mitochondrial disorder due to a dominant p. Y955H disease variant in DNA polymerase gamma

  • Siibak T
  • Clemente P
  • Bratic A
  • Bruhn H
  • Kauppila T
  • Macao B
  • Schober F
  • Lesko N
  • Wibom R
  • Naess K
  • Nennesmo I
  • Wedell A
  • Peter B
  • Freyer C
  • Falkenberg M
  • Wredenberg A
... View more Collapse

Human Molecular Genetics (p. 2515-2525) - 1/7/2017

10.1093/hmg/ddx146 View at source

  • ISSN 14602083

Cox25 teams up with Mss51, Ssc1, and Cox14 to regulate mitochondrial cytochrome c oxidase subunit 1 expression and assembly in Saccharomyces cerevisiae

  • Fontanesi F
  • Clemente P
  • Barrientos A

Journal Of Biological Chemistry (p. 555-566) - 7/1/2011

10.1074/jbc.m110.188805 View at source

  • ISSN 00219258

HCOA3 stabilizes cytochrome c oxidase 1 (COX1) and promotes cytochrome c oxidase assembly in human mitochondria

  • Clemente P
  • Peralta S
  • Cruz-Bermudez A
  • Echevarría L
  • Fontanesi F
  • Barrientos A
  • Fernandez-Moreno M
  • Garesse R
... View more Collapse

Journal Of Biological Chemistry (p. 8321-8331) - 22/3/2013

10.1074/jbc.m112.422220 View at source

  • ISSN 00219258

Coiled coil domain-containing protein 56 (CCDC56) is a novel mitochondrial protein essential for cytochrome c oxidase function

  • Peralta S
  • Clemente P
  • Sánchez-Martínez A
  • Calleja M
  • Hernández-Sierra R
  • Matsushima Y
  • Adán C
  • Ugalde C
  • Fernández-Moreno MA
  • Kaguni LS
  • Garesse R
... View more Collapse

Journal Of Biological Chemistry (p. 24174-24185) - 13/7/2012

10.1074/jbc.m112.343764 View at source

  • ISSN 00219258

Mutations in the mitochondrial tryptophanyl-tRNA synthetase cause growth retardation and progressive leukoencephalopathy

  • Maffezzini C
  • Laine I
  • Dallabona C
  • Clemente P
  • Calvo-Garrido J
  • Wibom R
  • Naess K
  • Barbaro M
  • Falk A
  • Donnini C
  • Freyer C
  • Wredenberg A
  • Wedell A
... View more Collapse

Molecular Genetics & Genomic Medicine - 1/6/2019

10.1002/mgg3.654 View at source

  • ISSN 23249269

Myoglobinopathy is an adult-onset autosomal dominant myopathy with characteristic sarcoplasmic inclusions

  • Olive, Montse
  • Engvall, Martin
  • Ravenscroft, Gianina
  • Cabrera-Serrano, Macarena
  • Jiao, Hong
  • Bortolotti, Carlo Augusto
  • Pignataro, Marcello
  • Lambrughi, Matteo
  • Jiang, Haibo
  • Forrest, Alistair R. R.
  • Benseny-Cases, Nuria
  • Hofbauer, Stefan
  • Obinger, Christian
  • Battistuzzi, Gianantonio
  • Bellei, Marzia
  • Borsari, Marco
  • Di Rocco, Giulia
  • Viola, Helena M.
  • Hoo, Livia C.
  • Cladera, Josep
  • Lagerstedt-Robinson, Kristina
  • Xiang, Fengqing
  • Wredenberg, Anna
  • Miralles, Francesc
  • Jose Baiges, Juan
  • Malfatti, Edoardo
  • Romero, Norma B.
  • Streichenberger, Nathalie
  • Via, Christophe
  • Claeys, Kristl G.
  • Straathof, Chiara S. M.
  • Goris, An
  • Freyer, Christoph
  • Lammens, Martin
  • Bassez, Guillaume
  • Kere, Juha
  • Clemente, Paula
  • Sejersen, Thomas
  • Udd, Bjarne
  • Vidal, Noemi
  • Ferrer, Isidre
  • Edstrom, Lars
  • Wedell, Anna
  • Laing, Nigel G.;
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Nature Communications - 1/12/2019

10.1038/s41467-019-09111-2

  • ISSN 20411723
  • iMarina

This researcher has no books.

Mitochondrial DNA replication in health and disease

  • Gallardo, María Esther
  • Clemente Pérez, Paula
  • Echevarría Zamora, Lucía
  • Peralta, Susana
  • Garesse, Rafael

Mitochondrial Pathophysiology (p. 115-143) - 1/1/2011

  • iMarina

This researcher has no conferences.

This researcher has no working papers.

This researcher has no technical reports.

Caracterización funcional de defectos del sistema de fosforilación oxidativa causantes de enfermedades mitocondriales.

  • Maria Carmen Prior de Castro (Investigador/a)
  • Rosana Hernandez Sierra (Investigador/a)
  • Clemente Perez, Paula (Investigador/a)
  • Fernandez Moreno, Miguel Angel (Investigador/a)
  • Gallardo Perez, Maria Esther (Investigador/a)
  • Carmen Prior Castro (Investigador/a)
  • Carmen Garcia Vallejo (Investigador/a)
  • Garesse Alarcon, Rafael (Investigador principal (IP))
... View more Collapse

Period: 01-01-2011 - 31-12-2013

  • iMarina

Acción coordinada para el estudio de los mecanismos determinantes de la expresión fenotípica de mutaciones en genes reguladores del sistema de fosforilación oxidativa (parte 3: variabilidad genotípica del MTDNA y defectos de.

  • González Vioque, Emiliano (Investigador/a)
  • Sánchez Martínez, Álvaro (Investigador/a)
  • Echevarria Zamora, Lucia (Investigador/a)
  • Clemente Perez, Paula (Investigador/a)
  • Veronica Domingo Rodriguez (Investigador/a)
  • Rosana Hernandez Sierra (Investigador/a)
  • Fernandez Moreno, Miguel Angel (Investigador/a)
  • Gallardo Perez, Maria Esther (Investigador/a)
  • Isabel Sanjuan Bilbao (Investigador/a)
  • Carmen Garcia Vallejo (Investigador/a)
  • Garesse Alarcon, Rafael (Investigador principal (IP))
... View more Collapse

Period: 01-01-2008 - 31-12-2010

  • iMarina

CCDC56, una proteína esencial para la formación de la citocromo c oxidasa en células humanas

  • Clemente Perez, Paula (Autor o Coautor)
  • Garesse Alarcon, Rafael (Director)
  • Fernandez Moreno, Miguel Angel (Director)
  • Fernandez Piqueras, Jose (Autor o Coautor) Doctorando: CLEMENTE PEREZ, PAULA

20/4/2012

  • iMarina

This researcher has no patents or software licenses.

Last data update: 3/18/24 11:33 AM