Satrustegui Gil Delgado, Jorgina jorgina.satrustegui@uam.es
Publications
- Articles 148
- Books 1
- Book chapters 1
- Conferences 10
- Working papers 1
- Technical reports 0
- Research projects 13
- Supervised theses 55
- Patent or software license 1
Regulation of neuronal energy metabolism by calcium: Role of MCU and Aralar/malate-aspartate shuttle
- del Arco, A
- González-Moreno, L
- Pérez-Liébana, I
- Juaristi, I
- González-Sánchez, P
- Contreras, L
- Pardo, B
- Satrústegui, J
Biochimica Et Biophysica Acta-Molecular Cell Research (p. 119468-119468) - 1/6/2023
- ISSN 01674889
- iMarina
Exogenous aralar/slc25a12 can replace citrin/slc25a13 as malate aspartate shuttle component in liver
- González-Moreno, L
- Santamaría-Cano, A
- Paradela, A
- Martínez-Chantar, ML
- Martín, MA
- Pérez-Carreras, M
- García-Picazo, A
- Vázquez, J
- Calvo, E
- González-Aseguinolaza, G
- Saheki, T
- del Arco, A
- Satrústegui, J
- Contreras, L
Molecular Genetics And Metabolism Reports (p. 100967-100967) - 1/6/2023
- ISSN 22144269
- iMarina
A Ca2+-Dependent Mechanism Boosting Glycolysis and OXPHOS by Activating Aralar-Malate-Aspartate Shuttle, upon Neuronal Stimulation
- Pérez-Liébana I, Juaristi I, González-Sánchez P, González-Moreno L, Rial E, Podunavac M, Zakarian A, Molgó J, Vallejo-Illarramendi A, Mosqueira-Martín L, Lopez de Munain A, Pardo B, Satrústegui J, Del Arco A
Journal Of Neuroscience (p. 3879-3895) - 11/5/2022
10.1523/jneurosci.1463-21.2022
- ISSN 15292401
- iMarina
AGC1 Deficiency: Pathology and Molecular and Cellular Mechanisms of the Disease
- Pardo B
- Herrada-Soler E
- Satrústegui J
- Contreras L
- Del Arco A
International Journal Of Molecular Sciences - 1/1/2022
10.3390/ijms23010528 View at source
- ISSN 14220067
Mitochondria and calcium defects correlate with axonal dysfunction in GDAP1-related Charcot-Marie-Tooth mouse model
- Civera-Tregón A
- Domínguez L
- Martínez-Valero P
- Serrano C
- Vallmitjana A
- Benítez R
- Hoenicka J
- Satrústegui J
- Palau F
Neurobiology Of Disease - 1/5/2021
10.1016/j.nbd.2021.105300 View at source
- ISSN 1095953X
Effective therapeutic strategies in a preclinical mouse model of Charcot-Marie-Tooth disease
- Nuevo-Tapioles, Cristina
- Santacatterina, Fulvio
- Sanchez-Garrido, Brenda
- de Arenas, Cristina Nunez
- Robledo-Bergamo, Adrian
- Martinez-Valero, Paula
- Cantarero, Lara
- Pardo, Beatriz
- Hoenicka, Janet
- Murphy, Michael P.
- Satrustegui, Jorgina
- Palau, Francesc
- Cuezva, Jose M.;
Human Molecular Genetics (p. 2441-2455) - 15/12/2021
10.1093/hmg/ddab207 View at source
- ISSN 14602083
βOHB Protective Pathways in Aralar-KO Neurons and Brain: An Alternative to Ketogenic Diet
- Pérez-Liébana I
- Casarejos MJ
- Alcaide A
- Herrada-Soler E
- Llorente-Folch I
- Contreras L
- Satrústegui J
- Pardo B
Journal Of Neuroscience (p. 9293-9305) - 25/11/2020
10.1523/jneurosci.0711-20.2020 View at source
- ISSN 15292401
Extracellular ATP and glutamate drive pyruvate production and energy demand to regulate mitochondrial respiration in astrocytes
- Juaristi I
- Llorente-Folch I
- Satrústegui J
- del Arco A
Glia (p. 759-774) - 1/4/2019
10.1002/glia.23574 View at source
- ISSN 08941491
Mitochondrial movement in Aralar/Slc25a12/AGC1 deficient cortical neurons
- Puertas-Frías G, Del Arco A, Pardo B, Satrústegui J, Contreras L
Neurochemistry International - 1/12/2019
- ISSN 01970186
- iMarina
The Response to Stimulation in Neurons and Astrocytes
- Juaristi I., Contreras L., González-Sánchez P., Pérez-Liébana I., González-Moreno L., Pardo B., del Arco A., Satrústegui J.
Neurochemical Research (p. 2385-2391) - 1/10/2019
10.1007/s11064-019-02803-7 View at source
- ISSN 03643190
Role of calcium regulated mitochondrial metabolite transporters in calcium signalling and neuronal respiration
- Satrustegui, J.
- Gonzalez-Sanchez, P.
- Contreras, L.
- Perez-Liebana, I.
- Juaristi, I.
- del Arco, A.
- Pardo, B.;
Febs Open Bio (p. 25-25) - 1/1/2019
- ISSN 22115463
- iMarina
LACK OF GDAP1 IN MOTOR NEURONS REVEALS IMPAIRMENT IN MITOCHONDRIAL DYNAMICS AND CALCIUM HOMEOSTASIS IN THE CHARCOT-MARIE-TOOTH DISEASE PATHOGENESIS
- Civera-Tregon, A.
- Juarez, P.
- Fernandez-Lizarbe, S.
- Pla-Martin, D.
- Martinez-Valero, P.
- Satrustegui, J.
- Palau, F.;
Journal Of The Peripheral Nervous System (p. 244-244) - 1/1/2016
- ISSN 10859489
- iMarina
Role of the Ca2+ uniporter and the mitochondrial Ca2+-activatedtransporters of aspartate/glutamate (aralar/AGC1) and ATP-Mg/Pi(SCaMC-3) in agonist-stimulated respiration of intact cerebral cortexneurons
- Rueda, Carlos B.
- Llorente-Folch, Irene
- Traba, Javier
- Amigo, Ignacio
- del Arco, Araceli
- Pardo, Beatriz
- Satrustegui, Jorgina;
Biochimica Et Biophysica Acta-Bioenergetics (p. S80-S81) - 1/1/2012
10.1016/j.bbabio.2012.06.219 View at source
- ISSN 00052728
Calcium Signaling in Neuronal Mitochondria
- Satrustegui, Jorgina
- Llorente-Folch, Irene
- Contreras, Laura
- Marmol, Patricia
- Cavero, Santiago
- Traba, Javier
- Amigo, Ignacio
- Rueda, Carlos
- Del Arco, Araceli
- Pardo, Beatriz;
Journal Of General Physiology (p. 12A-12A) - 1/7/2011
- ISSN 00221295
- iMarina
Risk-Adapted Treatment in Clinical Stage I Testicular Seminoma: The Third Spanish Germ Cell Cancer Group Study
- Aparicio, Jorge
- Maroto, Pablo
- Garcia del Muro, Xavier
- Guma, Josep
- Sanchez-Munoz, Alfonso
- Margeli, Mireia
- Domenech, Montserrat
- Bastus, Roma
- Fernandez, Antonio
- Lopez-Brea, Marta
- Terrassa, Josefa
- Meana, Andres
- Martinez del Prado, Purificacion
- Sastre, Javier
- Satrustegui, Juan J.
- Girones, Regina
- Robert, Lidia
- Germa, Jose R.;
Journal Of Clinical Oncology (p. 4677-4681) - 10/12/2011
10.1200/jco.2011.36.0503 View at source
- ISSN 0732183X
The Ca2+-dependent ATP-Mg/Pi carriers as novel regulators of themitochondrial permeability transition pore
- Traba, Javier
- Amigo, Ignacio
- Rueda, Carlos
- Szabadkai, Gyorgy
- Duchen, Michael R.
- Satrustegui, Jorgina
- del Arco, Araceli;
Biochimica Et Biophysica Acta-Bioenergetics (p. 130-130) - 1/1/2010
10.1016/j.bbabio.2010.04.386 View at source
- ISSN 00052728
Role of aralar, the mitochondrial transporter of aspartate-glutamate, in brain N-acetylaspartate formation and Ca2+ signaling in neuronal mitochondria
- Satrústegui J., Contreras L., Ramos M., Marmol P., Del Arco A., Saheki T., Pardo B.
Journal Of Neuroscience Research (p. 3359-3366) - 15/11/2007
10.1002/jnr.21299 View at source
- ISSN 03604012
Protection by pyruvate and malate against glutamate-mediated neurotoxicity does not involve mitochondrial energization
- Bogonez, E
- Ruiz, F
- Alvarez, G
- Pereira, R
- Hernandez, M
- Villalba, M
- Cruz, F
- Cerdan, S
- Satrustegui, J
Faseb Journal (p. A1261-A1261) - 1/12/1997
- ISSN 08926638
- iMarina
Cytosolic and mitochondrial calcium in synaptosomes during aging
- Satrustegui, J
- Villalba, M
- Pereira, R
- Bogonez, E
- MartinezSerrano, A;
Life Sciences (p. 429-434) - 3/7/1996
10.1016/0024-3205(96)00322-0 View at source
- ISSN 00243205
Whole-exome sequencing identifies MDH2 as a new familial paraganglioma gene
- Cascón A, Comino-Méndez I, Currás-Freixes M, de Cubas AA, Contreras L, Richter S, Peitzsch M, Mancikova V, Inglada-Pérez L, Pérez-Barrios A, Calatayud M, Azriel S, Villar-Vicente R, Aller J, Setién F, Moran S, Garcia JF, Río-Machín A, Letón R, Gómez-Graña Á, Apellániz-Ruiz M, Roncador G, Esteller M, Rodríguez-Antona C, Satrústegui J, Eisenhofer G, Urioste M, Robledo M
Jnci-Journal Of The National Cancer Institute - 1/5/2015
10.1093/jnci/djv053 View at source
- ISSN 00278874
This researcher has no technical reports.
Análisis genómico, transcriptómico, proteómico y funcional de la mitocondria y su incidencia en patología humana
- Garesse Alarcon, Rafael (Investigador principal (IP))
- Vinos Gomez de Balugera Javier (Investigador/a)
- Cadenas Alvarez, Susana (Investigador/a)
- Santiago Rodriguez de Córdoba (Investigador/a)
- Marco Cuellar, Roberto (Investigador/a)
- Miguel Angel Martin Casanueva (Investigador/a)
- Fernandez Moreno, Miguel Angel (Investigador/a)
- Maria del Mar Gonzalez Barroso (Investigador/a)
- Cervera Jover, Margarita (Investigador/a)
- Margarita Campos Gonzalez (Investigador/a)
- Cuezva Marcos, Jose Manuel (Investigador/a)
- Richard Rodriguez, Eva Maria (Investigador/a)
- Belen Bornstein (Investigador/a)
- Aranzazu Sanchez Muñoz (Investigador/a)
- Satrustegui Gil Delgado, Jorgina (Coordinador/a)
Period: 01-01-2006 - 31-12-2010
- iMarina
Funciones de los transportadores mitocondriales dependientes de calcio: los transportadores de aspartato-glutamato (AGCS) y de ATP-MG/PI (SCAMCS O APCS)
- Patricia Marmol Carrasco (Investigador/a)
- Javier Traba Dominguez (Investigador/a)
- Laura Contreras Balsa (Investigador/a)
- Pardo Merino, Beatriz (Investigador/a)
- Barbara Sese Cobos (Investigador/a)
- Satrustegui Gil Delgado, Jorgina (Investigador principal (IP))
Period: 31-12-2005 - 30-12-2008
- iMarina
Papel de la mitocondria en la muerte neuronal: estudio de la implicación de aralar y la lanzadera Nadh Malato-Aspartato en la susceptibilidad a la muerte neuronal.
- Patricia Marmol Carrasco (Investigador/a)
- Pardo Merino, Beatriz (Investigador/a)
- Araceli del Arco Martinez (Investigador/a)
- Satrustegui Gil Delgado, Jorgina (Investigador principal (IP))
Period: 01-01-2005 - 31-12-2007
- iMarina
The mitochondrial aspartate-glutamate carrier Aralar/AGC1 controls neuronal respiration and (beta)-Hydroxybutyrate rescues brain defects caused by AGC1 deficiency
- Satrustegui Gil Delgado, Jorgina (Director)
- Pardo Merino, Beatriz (Director) Doctorando: Pérez Liébana, Irene
30/6/2020
- iMarina
Tissue-specific expression of the atpase inhibitory factor 1 and its role in neuronal function
- Satrustegui Gil Delgado, Jorgina (Autor o Coautor)
- Cuezva Marcos, Jose Manuel (Director)
1/1/2020
- iMarina
Regulation of mitochondrial respiration |b role of Ca2+, ATP demand and pyruvate production
- Jorgina Satrústegui Gil-Delgado (Director)
- Araceli del Arco Martinez (Director) Doctorando: Inés Juaristi Santos
23/1/2019
- iMarina
Store-operated calcium entry in neural cells|ba role in Charcot-Marie-Tooth disease
- Jorgina Satrústegui Gil-Delgado (Director)
- Araceli del Arco Martinez (Director) Doctorando: Paloma González Sánchez
22/9/2017
- iMarina
Enfermedad de Charcot-Marie-Tooth asociada aGdap1 : alteraciones en nocicepción y señalización por calcio
- Satrústegui Gil-Delgado, Jorgina (Director)
- Contreras Balsa, Laura (Codirector)
15/9/2017
- iMarina
Regulation of the expression and function of mitochondrial uncoupling protein UCP3 in response to oxidative stress: involvement of the transcription factor Nrf2 and implications in cardiac ischemia-reperfusion
- Satrustegui Gil Delgado, Jorgina (Autor o Coautor)
- Cadenas Alvarez, Susana (Director) Doctorando: López Bernardo, Elia
1/1/2015
- iMarina
Regulación de la expresión y actividad de IF1, el inhibidor fisiológico de la H+-ATP sintasa de la mitocondria
- Satrustegui Gil Delgado, Jorgina (Autor o Coautor)
- Maria Sanchez Arago (Director)
- José Manuel Cuezva Marcos (Director) Doctorando: Javier García Bermúdez
1/1/2015
- iMarina
Brain alterations in lafora disease mouse models
- Satrustegui Gil Delgado, Jorgina (Autor o Coautor)
- Serratosa Fernandez, Jose Maria (Autor o Coautor)
- Bovolenta Nicolao, Paola (Codirector)
1/1/2015
- iMarina
Señalización por calcio a la mitocondria a través de CaMC
- Satrustegui Gil Delgado, Jorgina (Codirector)
- Pardo Merino, Beatriz (Codirector) Doctorando: Rueda Díez, Carlos B.
15/12/2014
- iMarina
Calcium modulation of mitochondrial function under physiological and pathological stimulation: Role of the atp-mg/pi carrier, scamc-3
- Cuezva Marcos, Jose Manuel (Autor o Coautor)
- Diaz Nido, Javier (Autor o Coautor)
- Satrustegui Gil Delgado, Jorgina (Autor o Coautor)
- Jorgina Satrústegui Gil-Delgado (Director)
- Beatriz Pardo Merino (Director)
- Araceli del Arco Martinez (Director) Doctorando: Carlos B Rueda Díez
1/1/2014
- iMarina
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